Proteinose alveolar pulmonar
نویسندگان
چکیده
INTRODUÇÃO: A Proteinose Alveolar Pulmonar (PAP) é uma síndrome rara causada pelo acúmulo de surfactante no espaço alveolar, mais comumente encontrada em homens com idade média 20 a 50 anos. É patologia apresentação clínica variável e difícil diagnóstico, que pode cursar dispneia, tosse dor torácica. APRESENTAÇÃO DO CASO: RSM, sexo masculino, 39 anos, ex-tabagista um maço por dia, durante 8 queixa torácica, ventilatório dependente, febre não aferida esporadicamente, seca, raramente produtiva manhã, cianose extremidades aos esforços há 4 meses. Após 6 meses, evoluiu piora do quadro. Prosseguiu investigação pneumopatia extensa bilateral, realização biópsia pulmonar, confirmando o diagnóstico PAP. DISCUSSÃO: tomografia tórax exame inicial ser solicitado na PAP, seguido da confirmação líquido lavado broncoalveolar. Embora seja obrigatório, padrão-ouro pulmonar cirúrgica. O principal tratamento lavagem além fisioterapia suporte pulmonar. CONCLUSÃO: Ainda doença rara, essencial diferencial PAP quadros dispneia crônica progressiva, explicadas outras patologias prevalentes.
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ژورنال
عنوان ژورنال: Brazilian Journal of Health Review
سال: 2022
ISSN: ['2595-6825']
DOI: https://doi.org/10.34119/bjhrv5n5-039